GENERAL INFORMATION
Ø News
Ø General Health Info
Ø Radiology & Oncology
Ø Breast Health Info Centre
Ø Palliative Care & Cancer Support
Ø The College Of Radiology
Ø Directories

Our patient briefings explain a variety of diagnostic procedures and treatments, how patients should prepare for them, and what patients can expect to experience during and after the procedure. These briefings are provided as a service to help patients address their medical care with less anxiety and greater comfort.

PILIHAN BAHASA MALAYSIA
Ø Ke Seksyen BM
Ø Pusat Sumber Kanser Payudara

Click Here! With the introduction of the new Agfa film/screen system for mammography, we have taken mammography another major step forward. This new milestone in mammography incorporates a century of experience in imaging technology, offering an image with high contrast and high definition for outstanding visualization of details throughout the breast.

MEDICAL & RADIOLOGY PROFESSIONALS
Ø Click here, if you are a medical or radiology professional

TALKBACK (Q&A)
Ø Radiology Malaysia Forum
Ø Having Problems using this website?
Ø Q & A Archive
Ø Send Your Feedback

MEMBERS' CORNER

Restricted Zone
Ø Register for Access
Ø Members' Homepage
Ø JobSearch
Ø Suara Radiologi/College Newsletter


Interested in sponsoring this section? Please click here for more info

You may also place advertisements throughout the Radiology Malaysia web site. For more information on how you may do this, please click here!
 

Media Centre
Information about the College of Radiology and its activities for the Media and Press.
Please Click Here!
 

This web site is best viewed at 1024 x 768 resolution using:

Windows Internet Explorer 7

OR



You should also set your display to show 16M colours for better colour reproduction.



For a complete Web Experience!

Whilst every effort is taken to ensure that information and other content on this site is as true and accurate as possible, there may be instances where errors may occur. In such an event, we should be grateful if you could notify us so that we can set the situation right.

We also take similar efforts to ensure that we do not infringe the rights of Copyright owners. Should you feel that we have committed a breach of copyright, please notify us so that we may arrange for the immediate removal of the material from this site.
 

 

Anti-Virus Info
 

Locations of visitors to this page
 

Case of the Month

by Dr Noreen Norfaraheen Lee Abdullah MD (UKM), MMed Radiology (UKM), AM(Mal)

Answer to Case Of the Month 
Fibrous Dysplasia of the Left Femur

Discussion of Findings
The shape of the upper end of left femur is deformed and has a configuration liken a shepherd’s crook. There is thinning of the bony cortex and expansion of the upper end of the left femur namely at the neck and the trochanters. Cystic lucencies with sclerotic margins occupy the medullary cavity at the upper end of left femoral shaft. The mid and distal shafts of the left femur are normal. The left femoral head is within the left hip joint and well covered by the acetabulum. Features are in keeping with fibrous dysplasia. Differential diagnoses include enchondromatosis, osteofibrous dysplasia, bone cysts, eosinophilic granuloma and non ossifying fibroma.

The diagnosis is Fibrous Dysplasia.
Fibrous Dysplasia (FD)
This condition is also known as the Lichtenstein Jaffe disease. It is a benign mesodermal disorder and affects the fibroosseous development which manifest as a defect in osteoblastic differentiation and maturation. It affects male and female alike with 75% presenting before the age of 30 years old. The peak age of presentation is between 3 and 15 years.

There are three types of FD - Monostotic, polyostotic and craniofacial forms.

Monostotic form is also known as the localized type and is more common (70–80%). The patients are usually asymptomatic until the 2nd or 3rd decade. One bone is normally involved and this form usually affects the ribs and proximal femur.

The polyostotic form presents earlier in life, usually in the first decade. The usual presentation will be leg pain, limp, pathological fracture or limb length discrepancy. The femur is usually affected (90%), tibia (81%), pelvis (78%) and foot (73%). The ribs, spine and clavicle are also affected but the incidence is less. Sometimes other disorders are present especially endocrinopathies such as hyperthyroidism, acromegaly, hyperparathyroidism, Cushing syndrome or rickets. McCune Albright syndrome is one such example whereby the patient has polyostotic fibrous dysplasia, skin pigmentation, accelerated skeletal maturation and precocious puberty.

The craniofacial form is rare and is known as leontiasis ossea. The cranial bones usually involved are sphenoid, frontal, maxillary, ethmoid, occipital and temporal bones in decreasing order of frequency.

Transformation into osteo/chondro/fibro sarcoma or malignant fibrous histiocytoma has been reported. The manifestation is increasing pain and the radiographic features are that of a pathological fracture with enlarging soft tissue mass and lytic lesions.

A skeletal survey is required when first discovered. The patient should be on long term follow up and radiographs at yearly intervals would be appropriate for surveillance and early detection of complications.

Reference: Wolfgang Dahnert – Radiology Review Manual
 
About the Author 
Dr Noreen, a Consultant Radiologist is currently with the Universiti Sains Malaysia, Kubang Kerian, Kelantan, Malaysia.
 
Discuss This Case in the Forum
If you wish to ask questions and discuss this case in our Forum, please click here!

 

Please click here for more cases!
 

 

Copyright © 2001-2008 College of Radiology, Academy of Medicine of Malaysia
All Rights Reserved

Terms of Use

Last Updated:
Sunday, 17 August 2008